2021 Type and Severity Summary of Identified Cases of Hearing Loss

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Data Source: 2021 CDC Early Hearing Detection and Intervention (EHDI) Hearing Screening & Follow-up Survey (HSFS)

Background: CDC’s National Center on Birth Defects and Developmental Disabilities promotes the health of babies, children, and adults, with a focus on preventing birth defects and developmental disabilities and optimizing the health outcomes of people with disabilities. As part of these efforts, the center is actively involved in addressing the early identification of permanent hearing loss among newborns and infants.

Hearing loss affects between 1 and 2 per 1,000 infants in the United States and, when left undetected or untreated, can delay a child’s speech and language, social, and emotional development.1 To ensure children with permanent hearing loss are identified and receive services as soon after birth as possible, states and territories have implemented Early Hearing Detection and Intervention (EHDI) programs. These EHDI programs work to ensure all infants

  • Are screened for hearing loss, by 1 month of age
  • Receive diagnostic, audiologic evaluation (for those not passing the screening), by 3 months of age
  • Are enrolled in early intervention (for those identified with permanent hearing loss), by 6 months of age2

The Hearing Screening & Follow-up Survey (HSFS) is a voluntary survey sent out annually by CDC to each jurisdictional EHDI program. It requests aggregated hearing information on infants born in a specified calendar year (e.g., 2021). The survey helps to assess the progress of EHDI efforts to identify infants with permanent hearing loss across the United States.

This summary highlights type, severity, and laterality of permanent hearing loss for babies born between January 1, 2021 and December 31, 2021. Categories of severity are based on the American Speech-Language-Hearing Association (ASHA) classification system for hearing loss. The ASHA categories are as follows:

ASHA Categories
Degree of Hearing Loss Hearing loss range (dB HL)
Normal

-10 to 15

Slight

16 to 25

Mild

26 to 40

Moderate

41 to 55

Moderately severe

56 to 70

Severe

71 to 90

Profound

91+

 

Number of Survey Respondents Who Provided Type and Severity Data: 52α (48 states, 3 territories, 1 district) AK, AZ, AR, CA, CO, Commonwealth of the Northern Mariana Islands, CT, DE, District of Columbia, FL, GA, Guam, HI, ID, IL, IN, IA, KS, KY, LA, ME, MD, MA, MI, MN, MO, MT, NE, NV, NH, NJ, NM, NY, NC, ND, OH, OK, OR, PA, Puerto Rico, RI, SC, SD, TN, TX, UT, VT, VA, WA, WV, WI, WY

2020 Type and Severity Summary of Identified Cases of Hearing Loss (By Ear):ASHA Classification
Total Number of Reported Infants with Hearing Loss, 2021 CDC EHDI HSFS 6,520 Children
BILATERAL (by Ear) UNILATERAL (by Ear) LATERALITY UNKNOWN (i.e., Unknown if case is a unilateral or bilateral loss)
RIGHT EAR LEFT EAR UNKNOWN EAR (degree of loss for each ear) RIGHT EAR LEFT EAR UNKNOWN EAR

Sensorineural

Slight

33

31

0

0

13

11

0

1

Mild

595

592

0

0

98

106

0

0

Moderate

697

681

0

0

90

114

0

2

Moderately Severe

279

294

0

0

56

68

0

2

Severe

242

240

0

0

85

80

0

2

Profound

526

537

0

0

166

162

0

1

Unknown Severity

62

69

0

0

23

20

0

70

Conductive

Slight

76

6

0

0

4

1

0

0

Mild

70

62

0

0

33

33

0

0

Moderate

92

90

0

0

100

68

0

1

Moderately Severe

85

85

0

0

187

88

0

0

Severe

34

30

0

0

47

41

0

1

Unknown Severity

48

50

0

0

90

44

0

16

Mixed

Slight

1

4

0

0

1

0

0

0

Mild

43

41

0

0

6

8

0

0

Moderate

76

85

0

0

14

27

0

1

Moderately Severe

81

85

0

0

27

25

0

1

Severe

58

49

0

0

23

21

0

0

Profound

24

33

0

0

11

7

0

0

Unknown Severity

20

20

0

0

8

3

0

11

Type Unknown

Slight

13

16

0

0

5

11

0

0

Mild

66

76

0

0

31

23

0

16

Moderate

58

64

0

0

9

23

1

18

Moderately Severe

27

36

0

0

16

18

0

3

Severe

29

15

0

0

7

8

0

0

Profound

31

31

0

0

6

7

0

6

Unknown Severity

96

79

2

2

37

30

1

257

Auditory Neuropathy

Slight

1

0

0

0

0

0

0

0

Mild

4

3

0

0

0

0

0

0

Moderate

1

1

0

0

4

7

0

0

Moderately Severe

4

2

0

0

0

2

0

0

Severe

11

9

0

0

2

8

0

0

Profound

20

21

0

0

17

19

0

0

Unknown Severity

125

126

0

0

42

50

0

1

Totals by Ear

3,559

3,563

2

2

1,258

1,133

2

410

Totals by Child

3,561

2

1,258

1,133

2

410

Laterality Totals (by Child)

3,563 Bilateral Cases

2,393 Unilateral Cases

 

Total all Types and Severity (by Child)

6,366

Cases Resolved (i.e., hearing loss to no hearing loss)

154

Overall Total (by Child)

6,520

Summary of Type and Severity of Identified Cases of Hearing Loss in 2021

References

1American Speech-Language-Hearing Association (ASHA). Effects of hearing loss on development. Available at: https://www.asha.org/public/hearing/effects-of-hearing-loss-on-development.
Accessed April 8, 2021

2Year 2019 Position Statement: Principles and Guidelines for Early Hearing Detection and Intervention Programs (2019). Journal of Early Hearing Detection and Intervention, 4(2), 1-44. https://digitalcommons.usu.edu/jehdi/vol4/iss2/1/

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