Other Eye Disorders – Other Retinal Disorders

Diagnosed Prevalence

VEHSS identifies the annual prevalence of diagnosed Other Retinal Disorders based on the presence of International Classification of Diseases (ICD)-9 and ICD-10 codes in patient claims or electronic health record (EHR) systems. Patients with one or more diagnosis codes associated with a VEHSS subgroup are assigned to that subgroup. Diagnosis codes may be primary or secondary. Only one instance of a diagnosis code is required for assignment to the subgroup. Note that diagnosis codes in claims data are intended for billing purposes. Codes may not be present in cases where diagnosis codes are not required to justify payment. Diagnosed prevalence will also not identify any undiagnosed conditions, will not include patients not covered by the insurer, and will not identify prevalence among patients without a visit in the calendar year of data.

Diagnosed other retinal disorders include a patient having one or more diagnosis codes indicating one or more of the subgroups listed below.

Sample Category and Subgroup Definitions
Subgroup Indicated conditions
Other retinal disorders, any stage Category total – includes any clinical stage below.
Retina vascular disease, occlusive (arterial, venous)​ Retina vascular disease, occlusive (arterial, venous) includes diagnosis codes indicating unspecified or transient retinal vascular occlusion.
Central retinal vein occlusion Central retinal vein occlusion indicates diagnosis codes for central retinal vein occlusion, with or without macular edema or retinal neovascularization.
Branch retinal vein occlusion Branch retinal vein occlusion indicates diagnosis codes for tributary (branch) retinal vein occlusion, with or without macular edema or retinal neovascularization, or venous engorgement.
Central retinal arterial occlusion Central retinal arterial occlusion indicates diagnosis codes for central retinal arterial occlusion, with or without macular edema or retinal neovascularization.
Branch retinal artery occlusion Branch retinal artery occlusion indicates diagnosis codes for tributary (branch) retinal arterial occlusion.
Retina vascular disease, non-occlusive Retina vascular disease, non-occlusive includes diagnosis codes indicating hypertensive or exudative retinopathy, changes in retinal vascular appearance, retinal microaneurysms, retinal telangiectasis, neovascularization or vasculitis, intraretinal microvascular abnormalities, or unspecified background retinopathy.
Macular edema (cystoid or nondiabetic) Macular edema (cystoid or nondiabetic) indicates diagnosis codes for cystoid macular degeneration.
Hereditary chorioretinal dystrophy Hereditary chorioretinal dystrophy includes diagnosis codes indicating various types of chiorioretinal dystrophy, including circumpapillary, central choroidal atrophy, and choroideremia.
Myopic degeneration Myopic degeneration includes diagnosis codes indicating progressive high (degenerative) myopia.
Other/unspecified retinal disorders Other/unspecified retinal disorders include diagnosis codes indicating age-related choroidal atrophy, diffuse secondary atrophy of choroid, retinoschisis, retinal cysts, cyst of ora serrata, retinopathy of prematurity, nondiabetic proliferative retinopathy, unspecified separation of retinal layers, central serous chorioretinopathy, detachment of retinal pigment epithelium, macular cyst, hole, or pseudohole, toxic maculopathy, puckering of macula, various forms of retinal degeneration, retinal hemorrhage, and other or unspecified retinal disorders.

Full list of ICD-9 and ICD-10 codes [PDF – 2.1 MB].

Explore Data in the VEHSS Application

The data sources available for this category include Medicare (default), IRIS Registry, Medicaid, Managed Vision Care, and MarketScan commercial insurance claims. See data source documentation.