Prion disease incidence in the United State, 2003-2015 pdf icon[PDF – 295KB]external icon
Neurology® 2020;94:1-5. doi:10.1212/WNL.0000000000008680

Diagnostic and prognostic value of human prion detection in cerebrospinal fluid.external icon
Ann Neurol. 2017 Jan;81(1):79-92. doi: 10.1002/ana.24833.

Population screening for variant Creutzfeldt-Jakob disease using a novel blood test: diagnostic accuracy and feasibility study.
JAMA Neurology. April 2014;71(4)421-428.
This study indicates the prototype blood-based variant Creutzfeldt-Jakob (vCJD) disease assay has sufficient sensitivity and specificity to support using the assay to screen for vCJD infection in prion-exposed populations.

Detection of prion infectivity in variant Creutzfeldt-Jakob disease: a blood-based assay.
Lancet. February 2011;377:487-493.
These initial studies provide a prototype blood test for diagnosis of vCJD in symptomatic individuals, which could allow development of large-scale screening tests for asymptomatic vCJD infection.

Creutzfeldt-Jakob Disease Surveillance and Diagnosis pdf icon[PDF – 69KB]
Clinical Infectious Diseases. 2005;41:834–836. This article is in the public domain, and no copyright is claimed.

Creutzfeldt-Jakob Disease Not Related to a Common Venue – New Jersey, 1995 – 2004
MMWR. 2004;53(Early Release):1-4.

Creutzfeldt-Jakob Disease in Unusually Young Patients Who Consumed Venison.
Archives of Neurology, 2001;58:1673-1678.

Creutzfeldt-Jakob Disease in the United States: 1979-1998.
Journal of the American Medical Association. 2000;284(18).

Transmissible Spongiform Encephalopathies in Humans pdf icon[PDF – 183KB]
Annu. Rev. Microbiol. 1999;53:283–314.

Creutzfeldt-Jakob Disease Associated with Cadaveric Dura Mater Grafts.
MMWR. November 14, 1997;46(45):1066-1069.

Creutzfeldt-Jakob Disease in the United States, 1979-1994: Using National Mortality Data to Assess the Possible Occurrence of Variant Cases.
EID. October-December 1996;2(4):333-337.

Surveillance for Creutzfeldt-Jakob Disease
MMWR. August 9, 1996;45(31):665-668.

Links to Organizations outside CDC

California CJD Surveillance Projectexternal icon
The California CJD Surveillance Project conducts enhanced surveillance for CJD, variant CJD and other emerging forms of CJD in the state of California.

University of California, San Francisco: Memory and Aging Centerexternal icon
Creutzfeldt-Jakob Disease Website

Creutzfeldt-Jakob Disease Foundation, Inc.external icon

The UK Creutzfeldt-Jakob Disease Surveillance Unitexternal icon
University of Edinburgh, Scotland

Texas CJD Informationexternal icon
Texas Department of Health Services

WHO Infection Control Guidelines for Transmissible Spongiform Encephalopathies: Report of a WHO Consultation, Geneva, Switzerland, 23-26 March 1999external icon
From the World Health Organization (WHO).