For epidemiologic surveillance, CDC defines a case of KD as illness in a patient with fever of 5 or more days duration (or fever until the date of administration of intravenous immunoglobulin if it is given before the fifth day of fever), and the presence of at least 4 of the following 5 clinical signs:
- Cervical lymphadenopathy (at least 1.5 cm in diameter)
- Bilateral conjunctival injection
- Oral mucosal changes
- Peripheral extremity changes
Patients whose illness does not meet the above KD case definition but who have fever and coronary artery abnormalities are classified as having atypical or incomplete KD.